■骨骨异常增生是一种罕见的非遗传性疾病,其特征是在一个或多个骨phy中单侧占优势的骨软骨瘤,脚踝和膝盖是受影响最大的关节。治疗方法因疾病的定位而异,包括保守和手术选择。由于它的稀有性,缺乏明确的手术指南或具体的治疗方式.因此,本系统评价的目的是彻底调查骨phy发育不良,为管理这种情况提供循证指导,特别关注脚和脚踝。
■对PubMed和Cochrane图书馆进行了系统搜索,以确定所有已发表的与脚和踝关节骨phy半发育不良相关的文章。患者个人信息,比如性别,年龄,疾病类型,后续行动,本地化,临床表现,干预,和并发症,从每篇文章中系统地提取和分析。
■审查中包括25种合格出版物,共涉及70名患者(16名女性,53名男性)。平均年龄为9.6岁(SD7.3)。距骨是最普遍的位置,54%的病例的临床表现包括肿块和疼痛。92%的患者选择了外科手术,95%接受肿块切除.复发是最常见的并发症,在9%的病例中观察到。
■提高对发育不良的认识对于早期诊断和治疗至关重要,积极影响临床结果。在观测管理过程中,警惕监测至关重要,因为不受控制的质量增长会使外科手术复杂化。手术治疗以肿块切除为主,即使在年轻时也是可行的,但需要精确以防止复发或继发性关节炎。
■IV.
UNASSIGNED: Dysplasia epiphysealis hemimelica is a rare non-inherited condition characterized by the unilateral predominance of
osteochondromas in one or more epiphyses, with ankles and knees being the most affected joints. Treatment approaches vary based on the localization of the disease, encompassing both conservative and surgical options. Due to its rarity, there is a lack of definitive surgical guidelines or specific treatment modalities. Therefore, the objective of this systematic review was to thoroughly investigate dysplasia epiphysealis hemimelica to provide evidence-based guidance for managing this condition, specifically focusing on the foot and ankle.
UNASSIGNED: A systematic search was performed on PubMed and the Cochrane Library to identify all published articles related to dysplasia epiphysealis hemimelica of the foot and ankle. Individual patient information, such as gender, age, disease type, follow-up, localization, clinical presentation, intervention, and complications, were systematically extracted from each article and analyzed.
UNASSIGNED: Twenty-five eligible publications were included in the review, involving a total of 70 patients (16 females, 53 males). The mean age was 9.6 years (SD 7.3). The talus was the most prevalent location and clinical presentations included mass and pain in 54% of cases. Surgical procedures were chosen in 92% of patients, with 95% undergoing mass excision. Recurrence was the most frequent complication, observed in 9% of cases.
UNASSIGNED: Raising awareness about dysplasia epiphysealis hemimelica is crucial for early diagnosis and treatment, positively impacting clinical outcomes. Vigilant monitoring is essential during observational management, as unchecked mass growth can complicate surgical intervention. Surgical treatment focuses on mass excision, feasible even at a young age but requiring precision to prevent recurrence or secondary arthritis.
UNASSIGNED: IV.