特发性肺动脉高压是一种严重的疾病,预后不良。虽然劳力性呼吸困难是最常见的症状,心绞痛如胸痛,最常见的原因是右心室缺血,可能发生在晚期。我们介绍了一名有呼吸困难和心绞痛症状的肺动脉高压患者,其中计算机断层扫描血管造影显示左主冠状动脉被大的肺动脉瘤压迫。进行了经皮冠状动脉介入治疗和支架置入术,从而获得了显着的临床改善。此病例强调了不同心血管成像方式在诊断罕见疾病中的作用。
Idiopathic pulmonary arterial hypertension is a serious condition that carries a poor prognosis. While exertional dyspnea is the most common symptom, angina like chest pain, most often due to right ventricle ischemia, may occur at advanced stages. We present a patient with pulmonary hypertension symptomatic for dyspnea and angina in whom computed coronary tomography angiography showed compression of the left main coronary artery by a large pulmonary artery aneurysm. Percutaneous coronary intervention and stenting was performed resulting in significant clinical improvement. This case emphasizes the role of different cardiovascular imaging modalities for the diagnosis of rare conditions.