Hughes-Stovin综合征(HSS)是一种罕见的临床疾病,其特征是血栓性静脉炎以及多发性肺和支气管动脉瘤。它通常表现为咳嗽,呼吸困难,发烧,胸痛,咯血,其管理通常包括手术和医疗方法。在这份报告中,我们讨论一例HSS患者。一名30岁的男性患者因咯血入院。胸部CT评估后,观察双侧肺栓塞和肺动脉瘤。由于有口疮性病变的病史,Behçet病(BD)被认为是最初的诊断;然而,患者不符合标准,后来被诊断为HSS.开始静脉注射甲基强的松龙,以及环磷酰胺的维持治疗。在第四个月观察到治疗反应;然而,由于咯血的持续存在,后来需要额外的环磷酰胺循环,患者的病情稳定。HSS目前缺乏明确的诊断标准,需要进一步的研究来调查遗传背景,家族传输,和治疗替代方案。
Hughes-Stovin Syndrome (HSS) is a rare clinical condition characterized by thrombophlebitis as well as multiple pulmonary and bronchial aneurysms. It commonly presents with coughing, dyspnea, fever, chest pain, and hemoptysis, and its management usually consists of surgical and medical approaches. In this report, we discuss a case of a patient with HSS. A 30-year-old male patient was admitted to the pulmonary medicine ward for hemoptysis. After evaluation with chest CT, bilateral pulmonary embolism and pulmonary aneurysms were observed. Due to a history of aphthous lesions, Behçet\'s disease (BD) was considered the initial diagnosis; however, the patient did not fit the criteria and was later diagnosed with HSS. Intravenous methylprednisolone was initiated, along with a maintenance treatment with cyclophosphamide. Treatment response was observed in the fourth month; however, due to the persistence of hemoptysis, additional cycles of cyclophosphamide were later required, under which the patient\'s condition has been stable. HSS currently lacks clear diagnostic criteria, and further studies are needed to investigate genetic backgrounds, familial transmissions, and treatment alternatives.