未经证实:软骨粘液样纤维瘤是一种罕见的良性软骨肿瘤,良性软骨和纤维及粘液样组织的混合物。它通常影响年轻人,通常在生命的第二个和第三个十年,男性占主导地位。软骨粘液样纤维瘤的鉴别诊断,是巨细胞瘤,骨囊肿,内生软骨瘤,成骨细胞瘤,和低级软骨肉瘤.
方法:我们介绍一例18岁男性,自3年前以来,主要主诉右膝盖疼痛,三年内尺寸越来越大,直径达到55厘米。X线片和MRI显示溶血性扩张性多部位病变,有广阔的过渡带,右胫骨近端上骨干处骨膜反应。外科手术包括广泛切除,使用Kuntscher钉通过水泥膝关节固定术进行重建,动态压缩板,骨水泥和腓肠肌皮瓣。
未经批准:经过3个月的手术随访,没有复发的迹象,病人用拐杖部分负重行走。术后1年随访,肌肉骨骼肿瘤协会评分(MSTS)为80%。没有复发的迹象。
结论:在肿瘤体积较大的病例中,骨和软组织重建手术需要广泛切除作为机械和生物重建。水泥关节固定术提供了更快的手术持续时间,感染风险较低,和良好的功能结果。
UNASSIGNED: Chondromyxoid fibroma is a rare benign cartilaginous neoplasm, a mixture of benign cartilage and fibrous and myxoid tissue. It usually affects young people, commonly in the second and third decades of life with male being predominant. Differential diagnosess in chondromyxoid fibroma, are giant cell tumor, bone cyst, enchondroma, osteoblastoma, and low-grade chondrosarcoma.
METHODS: We present a case of an 18-years-old male, with chief complaint of pain on the right knee since 3 year ago with an increasing size reaching diameter of 55 cm within three years. The radiograph and MRI revealed lytic blastic expansile multiloculated lesion, with wide transitional zone, and periosteal reaction on the epymetadiaphyseal part of right proximal tibia. The surgical procedure was performed consist of wide excision, reconstruction by cement knee arthrodesis using Kuntscher-nail, dynamic compression plate, bone cement and gastrocnemius flap.
UNASSIGNED: After 3 months of surgery follow-up, there was no sign of recurrence, the patient walked partially weight bearing with a crutch. In 1 years post operative follow up, the Muscukoskeletal Tumor Society Scoring (MSTS) was 80%. There was no sign of recurrence.
CONCLUSIONS: In cases with large tumor size, wide excision with bone and soft tissue reconstructive surgery is required as mechanical and biological reconstruction. The cement arthrodesis provides a faster duration of surgery, lower risk of infection, and good functional outcome.