支气管扩张是一种传导气道的病理状态,在影像学上表现为支气管扩张的证据,在临床上表现为慢性生产性咳嗽。长期被认为是“孤儿病”,在发达国家和不发达国家,它仍然是发病率和死亡率的主要原因。随着医学领域的进步,伴随着疫苗和抗生素的广泛获得,改善卫生服务和更好地获得营养,支气管扩张的发病率明显下降,特别是在发达国家。这篇综述总结了目前与临床定义有关的知识,病因学,与小儿支气管扩张相关的临床方法和管理。
Bronchiectasis is a pathologic state of conducting airways manifested radiographically by evidence of bronchial dilation and clinically by chronic productive cough. Considered an \"orphan disease\" for long, it remains a major contributor to morbidity and mortality in both developed and underdeveloped countries. With the advances in the medical field accompanied by widespread access to vaccines and antibiotics, improved health services and better access to nutrition, the incidences of bronchiectasis have markedly decreased, particularly in developed countries. This review summarizes the current knowledge pertaining to the clinical definition, etiology, clinical approach and management related to pediatric bronchiectasis.