背景：先天性皮膜发育不全（MACC）在出生时表现为椭圆形表皮缺损。MACC的皮肤病变有各种临床表现。近年来,据报道，毛镜（头皮皮肤镜检查）对脱发疾病的有用性。然而,MACC的皮肤镜特征主要由病例报告报告。
目的：总结MACC的明显皮镜特征。
方法：这56例符合MACC临床诊断标准，无产钳分娩并发症或其他产伤。通过总结56张婴儿皮肤镜图，了解MACC的皮肤特征。
结果：MACC的皮肤镜表现的特征是毛囊开口和皮肤病变中心的毛发缺乏，半透明表皮，毛根和毛球沿皮肤病变边缘排列。
结论：MACC的典型皮肤镜特征有助于临床医生的早期诊断和鉴别诊断。
BACKGROUND: Membranous aplasia cutis congenita (MACC) presents at birth characterized by oval epidermis defect. Skin lesions with MACC have various clinic manifestations. In recent years, the usefulness of trichoscopy (scalp dermoscopy) has been reported for hair loss diseases. However, the dermoscopic features of MACC were mostly reported by case reports.
OBJECTIVE: To summarized the obvious dermoscopic characteristics of MACC.
METHODS: These 56 cases met the clinical diagnostic criteria for MACC without forceps delivery complications or other birth injuries. To find the dermoscopic characteristics of MACC by summarizing 56 infants\' dermoscopic pictures.
RESULTS: The dermoscopic manifestation of MACC are characterized by hair follicle openings and hair deficiency in the center of skin lesions, translucent epidermis, hair root and hair bulb arranged along the margins of skin lesion.
CONCLUSIONS: The typical dermoscopic characteristics of MACC could help clinicians to early diagnose and differential diagnosis.
