威廉姆斯综合征的严重主动脉病变有时可表现为最初的升主动脉病变。其次是更多的远端多水平梗阻和需要再次干预的复发。在这个系列中,一个早期,综合采用各种入路和灌注策略的综合手术方法取得了优异的长期效果.
Severe aortopathy in Williams syndrome can sometimes present with an initial ascending aortic pathology, followed in short order by more distal multilevel obstruction and recurrence requiring reintervention. In this series, an early, comprehensive surgical approach using a combination of various access and perfusion strategies yielded excellent long-term results.
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