弹性假性黄瘤（PXE）是一种进行性遗传性疾病，会影响皮肤等组织，视网膜,血管,和胃肠道。因此,需要针对特定器官的临床科室提供全面的医疗服务，以便为PXE患者提供最佳的临床实践。日本皮肤病协会制定的日本临床指南于2017年发布，旨在促进PXE相关医疗服务的平等可及性。这里,据报道，日本指南的英文版，并旨在成为PXE医疗的全球参考。
Pseudoxanthoma elasticum (PXE) is a progressive hereditary disease that affects tissues such as the skin, retina, blood vessels, and gastrointestinal tracts. Therefore, comprehensive medical care across clinical departments specialized in specific organs is needed to provide the best clinical practices to PXE patients. The Japanese version of clinical
guidelines developed by the Japanese Dermatological Association was published in 2017, and aimed to promote equal accessibility of PXE-related medical care. Here, the English version of Japanese
guideline is reported, and is intended to be worldwide reference for medical care of PXE.
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