成骨不全症(OI)是一种罕见的骨骼疾病,可增加患者对骨折的易感性。该人群中通常与骨折相关的一种并发症是不愈合的发生,导致假关节病。在这个系列中,在儿童OI人群中,有3例肱骨远端不愈合导致假关节炎。一个案例显示了成功的治疗尝试,一个案例是治疗失败的尝试,第三例患者拒绝接受治疗。此外,强调其他机构尝试的文献综述,成功,并介绍了治疗该临床实体的失败。结合从我们机构和其他机构检索到的数据,本综述表明,目前尚无治疗这些患者的标准.此外,基于本文提出的小案例系列和文献综述,无法概述儿科OI患者肱骨远端假性关节病治疗的明确指南。然而,我们的研究结果表明,对于无症状的肱骨远端假性关节炎患者,非手术治疗和手术治疗都可能是可行的选择.
Osteogenesis imperfecta (OI) is a rare skeletal disorder that increases a patient\'s susceptibility to bone fracture. One complication commonly associated with fractures in this population is the occurrence of non-union leading to pseudoarthrosis. In this
case series, three cases of non-union of the distal humerus leading to pseudoarthrosis in the pediatric OI population are presented. One
case presents a successful attempt at treatment, one
case presents a failed attempt at treatment, and the third
case presents a patient\'s refusal to get treated. Furthermore, a literature review highlighting other institutions\' attempts, successes, and failures at treating this clinical entity is presented. Combining the data retrieved from our institution and others, this review demonstrates that there is currently no standard for treating these patients. Additionally, based on the small
case series and literature review presented in this article, definitive guidelines for the treatment of pseudoarthrosis of the distal humerus in pediatric OI patients cannot be outlined. However, our findings suggest that both non-surgical and surgical treatments could be viable options for patients with asymptomatic pseudoarthrosis of the distal humerus.