孤立性纤维瘤（SFT）是一种罕见的间充质肿瘤，已知发生在各种软组织和内脏位置。肾脏是这些肿瘤的罕见部位之一，文献中约有64例。大多数肾脏SFT是棕白色的，固体,公司，未封装，和分叶肿块。在文献中从未报道过主要是囊性肾SFT。在此，我们描述了一名44岁男性的多囊性肾SFT病例，该病例具有特征性CD34/STAT6免疫表型。在处理肾脏和SFT的囊性梭形细胞肿瘤时，必须进行仔细的总体和显微镜检查，在鉴别诊断中应始终考虑SFT。STAT6免疫组织化学对于诊断相当特异。莫雷索,由于具有重要的治疗和预后意义，因此需要详细的免疫分析来排除其他肾脏梭形细胞肿瘤。
Solitary fibrous tumor (SFT) is a rare mesenchymal neoplasm known to occur at various soft tissue and visceral locations. Kidney is one of the rare locations for these tumors with around 64 cases being available in the literature. Most of the renal SFTs are tan-white, solid, firm, unencapsulated, and lobulated masses. A predominantly cystic renal SFT has never been reported in the literature. Herein we describe a case of
multicystic renal SFT in a 44-year-old male with the characteristic CD34 + /STAT6 + immunophenotype. A careful gross and microscopic examination is warranted while dealing with cystic spindle cell neoplasms of the kidney and SFT should always be considered in the differential diagnosis. STAT6 immunohistochemistry is quite specific for the diagnosis. Moreso, a detailed immunopanel is necessary to exclude other spindle cell neoplasms of the kidney because of significant therapeutic and prognostic implications.
