未经证实:Rosai-Dorfman-Destombes病(RDD)是一种病因不明的罕见组织增生性疾病。它通常发生在淋巴结中,并且可以影响结外组织和器官。肾RDD极为罕见,只有少数病例报告,其临床症状和影像学表现是非特异性的。迄今为止,在大量病例中没有文献总结其影像学表现。由于受累于不同的组织和器官,RDD没有标准治疗方法。据报道,肾脏受累的RDD患者预后不良。因此,对肾脏RDD的认识还需进一步深入。
UASSIGNED:我们在一名无症状的67岁男性中介绍了一例罕见的肾RDD病例。超声检查结果表明,两个肾脏都被低回声软组织病变包围,左肾有一个巨大的肿块,与肾包膜有清晰的边界。超声造影(CEUS)结果显示双侧肾周病变和肿块增强不足。然而,计算机断层扫描尿路造影(CTU)结果显示无明显增强。然后病人接受了一系列的实验室检查,但没有找到相关信息。为了做出明确的诊断,然后泌尿科医生切除了左肾周肿块和一些肾周组织,最终病理诊断为结外RDD。病人仍然无症状,到目前为止还没有治疗。
UNASSIGNED:该病例可能是第一例报告的行CEUS的病例,也是第二例无症状肾RDD的病例。根据以前的文献报道,我们发现肾RDD的一些特殊特征包括双侧肾周病变,表现为“毛状肾”。CEUS和/或CTU可用于帮助区分RDD的孤立肿块与常见肿瘤。避免误诊导致不必要的肾切除术。
UNASSIGNED: Rosai-Dorfman-Destombes disease (RDD) is a rare histioproliferative disease with unknown etiology. It commonly occurs in lymph nodes and can affect extra-nodal tissues and organs. Renal RDD is extremely rare, only a few cases have been reported, and its clinical symptoms and imaging findings are non-specific. To date, no literature has summarized its imaging manifestations in a large number of cases. Due to the involvement of different tissues and organs, there is no standard treatment for RDD. It has been reported that RDD patients with kidney involvement have a poor prognosis. Thus, understanding of renal RDD need to be extended.
UNASSIGNED: We present a rare
case of renal RDD in an asymptomatic 67-year-old male. The results of an ultrasound examination indicated that both kidneys were surrounded by hypoechoic soft tissue lesions, and there was a huge mass in the left kidney, which had a clear boundary with the renal capsule. The results of contrast-enhanced ultrasound (CEUS) showed hypo-enhancement in the bilateral perinephric lesions and mass. However, the computed tomography urography (CTU) findings revealed no obvious enhancement. The patient then underwent a series of laboratory tests, but no relevant information was found. To make a clear diagnosis, the urologist then removed the left perirenal mass and some perirenal tissues, and the patient was finally pathologically diagnosed with extra-nodal RDD. The patient remains asymptomatic, and no treatment has been administered to date.
UNASSIGNED: This
case may be the first reported
case in which CEUS was performed and the second reported
case of asymptomatic renal RDD. Based on the previous literature
reports, we found that some specific characteristics of renal RDD include bilateral perirenal lesions with a \"hairy kidney\" appearance. CEUS and/or CTU can be used to help differentiate a solitary mass of RDD from common tumors, to avoid misdiagnosis leading to unnecessary nephrectomy.