外周T细胞淋巴瘤（PTCL）是由成熟T细胞引起的一组异质性淋巴增殖性疾病，约占非霍奇金淋巴瘤的10％。PTCL-未指定是最常见的子类型，其次是血管免疫母细胞性T细胞淋巴瘤，间变性大细胞淋巴瘤,间变性淋巴瘤激酶阳性，间变性大细胞淋巴瘤,间变性淋巴瘤激酶阴性，和肠病相关T细胞淋巴瘤。本讨论部分的重点是T细胞淋巴瘤NCCN指南中概述的PTCL的诊断和治疗。
Peripheral T-cell lymphomas (PTCLs) are a heterogeneous group of lymphoproliferative disorders arising from mature T cells, accounting for about 10% of non-Hodgkin lymphomas. PTCL-not otherwise specified is the most common subtype, followed by angioimmunoblastic T-cell lymphoma, anaplastic large cell lymphoma, anaplastic lymphoma kinase-positive, anaplastic large cell lymphoma, anaplastic lymphoma kinase-negative, and enteropathy-associated T-cell lymphoma. This discussion section focuses on the diagnosis and treatment of PTCLs as outlined in the NCCN
Guidelines for T-Cell Lymphomas.
