并指畸形是手部最常见的先天性畸形,导致手指融合,并经常影响无名指和中指。发病率是2500名儿童中的1名,主要发生在男孩和高加索人。临床上,畸形可能表现为软组织或骨融合,导致手指的结合被表征为完整或不完整。这种融合可能涉及指骨,但也可能延伸到腕骨。甚至到掌骨或meta骨水平,很少到前臂和小腿的远端。畸形大多是孤立的,但可能与其他疾病或畸形一起发生,如滑膜症,杂音,裂口的手,clindactyly,或者多指。在Apert综合征的病例中可以观察到综合征综合征。波兰综合征,菲佛综合症,和许多其他人。2019年6月出生的女孩在出生时被诊断为右手先天性畸形-影响右中部,戒指,和小手指,分别。X射线成像后,确定了第三和第四近端指骨与掌骨的融合,形成与掌骨发育不全的临床结合的独特诊断。提倡手术干预,包括楔形截骨术,以纠正指骨基部的软骨病,以及背侧皮瓣,以关闭III和IV矫正期间产生的指间隙。手指。应用了梯形皮瓣,用于释放IV和V的连指。本文旨在介绍这种手术矫正及其有关非典型病例的结果。
Syndactyly is the most common congenital malformation of the hand, leading to the fusion of the digits and frequently affecting the ring and middle fingers. The incidence is 1 out of 2500 children, predominantly occurring in boys and Caucasians. Clinically, the malformation may present as a soft tissue or bony fusion, resulting in the union of the fingers characterised as complete or incomplete. This fusion may involve the phalanges but may also extend to the carpal/tarsal bones, even to the metacarpal or metatarsal level, rarely to the distal end of the forearm and lower leg. The malformation is mostly isolated but may occur together with other disorders or malformations such as synostosis, acro-syndactyly, cleft hand, clinodactyly, or polydactyly. Syndromic syndactyly can be observed in cases of Apert syndrome, Poland\'s syndrome, Pfeiffer syndrome, and many others. A girl born in June of 2019 was diagnosed with congenital malformation of the right hand at birth-affecting the right middle, ring, and little fingers, respectively. After X-ray imaging, the fusion of the third and fourth proximal phalanges to a common metacarpal was identified, forming a unique diagnosis of clino-syndactyly with metacarpal aplasia. Surgical intervention was advocated for, including a wedge osteotomy to correct the synchondrosis at the phalangeal base and a dorsal flap to close the interdigital space created during the correction of the III and IV. fingers. A trapezoid flap for the release of the syndactyly of the IV and V. fingers was applied. The paper aims to present this surgical correction and its results regarding an atypical
case of syndactyly with clinodactyly and metacarpal aplasia.