背景:肠重复囊肿很少见,此外,孤立性肠重复囊肿患病率较低。这些囊肿缺乏与胃肠道或邻近肠系膜脉管系统的连接,仅在10例病例报告中报告。在这些报告中,只有两份报告是恶性转化病例。我们的病例是孤立性肠重复囊肿晚期癌的报告。
方法:患者是一名43岁女性,有轻微腹痛和肿块形成。腹部对比增强计算机断层扫描显示右上腹膜腔存在130×100×90mm巨大的囊性肿块。囊性肿块具有增厚的壁和许多增强的结节。由于这些影像学发现表明肿瘤起源于胰腺,而术前诊断怀疑是粘液性囊性肿瘤。在手术发现中,肿瘤起源于胰头,未附着于胃肠道。最终病理显示囊肿为孤立性晚期肠重复囊肿癌,非胰腺来源。
结论:我们经历了一例极为罕见的完全孤立的晚期肠重复囊肿癌。这种情况的独特之处,术前诊断怀疑胰头粘液性囊性肿瘤,并进行了部分胰腺切除术。然而,在病理发现中,该囊肿诊断为晚期肠重复囊肿癌。
BACKGROUND: Enteric duplication cysts are rare and, in addition, isolated enteric duplication cysts are lower morbidity prevalence rate. These cysts lack a connection to the gastrointestinal tract or the adjacent mesenteric vasculature and have only been reported in 10
case reports. In these
reports, only two
reports were cases with malignant transformation. Our
case was a report for the advanced cancer of the isolated enteric duplication cyst.
METHODS: The patient was a 43 year-old woman with slightly abdominal pain and mass formation. The abdominal contrast-enhanced computed tomography showed 130 × 100 × 90 mm huge cystic mass existed in right upper peritoneal cavity. The cystic mass had thickened wall and many enhanced nodules. As these imaging findings suggested a tumor originated from pancreas and the preoperative diagnose was suspect of mucinous cystic neoplasm. In operative findings, the tumor originated from pancreatic head and did not attach to gastrointestinal tract. Final pathology indicated the cyst was an isolated advanced enteric duplication cyst cancer and not originated from pancreas.
CONCLUSIONS: We experienced an extremely rare
case of completely isolated advanced enteric duplication cyst cancer. Unique to this case, the preoperative diagnosis was suspect of mucinous cystic neoplasm arising from pancreas head and partial pancreatectomy was performed. However, in the pathological findings, this cyst diagnosed advanced enteric duplication cyst cancer.