PDF(Pubmed)
Abstract：
The pulmonary artery-to-left atrium (LA) fistula is one of the rare and unique structural causes of silent cyanosis. This correctable abnormality can be identified by having a high index of clinical suspicion and appropriate investigations using echocardiography and cardiac computed tomography (CT). We report an eight-year-old child who had worsening exertional dyspnea, long-standing central cyanosis, and recurrent infections. A large-sized fistula connecting the right pulmonary artery (RPA) to the LA with all the right- and left-sided pulmonary veins showed normal drainage into the LA, suggesting a type I RPA-to-LA fistula, which was diagnosed on cardiac CT. Percutaneous closure using the occluder device is planned as further management for the patient.
摘要：
肺动脉至左心房（LA）瘘是无症状紫癜的罕见且独特的结构原因之一。可以通过具有高的临床怀疑指数和使用超声心动图和心脏计算机断层扫描（CT）的适当检查来识别这种可校正的异常。我们报告了一个八岁的孩子，他的劳力性呼吸困难恶化，长期存在的中央紫癜，和反复感染。连接右肺动脉（RPA）和LA的大型瘘管，所有右和左肺静脉均显示出正常的LA引流，提示是I型RPA转LA瘘,心脏CT诊断出来的.计划使用封堵器装置的经皮闭合作为对患者的进一步管理。
