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Abstract：
BACKGROUND: Myelolipoma is an uncommon benign tumor composed of mature adipose tissue and hematopoietic elements. These tumors generally affect the adrenal glands, with anomalous presentations being rare and with few cases described in the literature. Most myelolipomas are asymptomatic and discovered incidentally, either through imaging tests or at autopsies. However, depending on the location and size of the lesion, myelolipomas can cause symptoms of mass effect. This article aims to report a very rare presentation of a symptomatic primary myelolipoma affecting the ribs.
METHODS: A 21-year-old white female patient presented with a complaint of burning chest pain over 3 months, with gradual worsening in intensity, accompanied by a progressively growing bulge in the right thoracic wall. The patient underwent thoracotomy of the fifth and sixth ribs with complete excision of the lesion with a safety margin. Thoracic wall reconstruction was performed using a polypropylene mesh. The patient had a good postoperative course and was discharged on postoperative day 3. Histopathological examination revealed a histological image consistent with myelolipoma.
CONCLUSIONS: This report underscores the importance of considering a myelolipoma diagnosis for tumor masses in the ribs.
METHODS: A 21-year-old white female patient presented with a complaint of burning chest pain over 3 months, with gradual worsening in intensity, accompanied by a progressively growing bulge in the right thoracic wall. The patient underwent thoracotomy of the fifth and sixth ribs with complete excision of the lesion with a safety margin. Thoracic wall reconstruction was performed using a polypropylene mesh. The patient had a good postoperative course and was discharged on postoperative day 3. Histopathological examination revealed a histological image consistent with myelolipoma.
CONCLUSIONS: This report underscores the importance of considering a myelolipoma diagnosis for tumor masses in the ribs.
摘要：
背景：髓质脂肪瘤是一种罕见的良性肿瘤，由成熟的脂肪组织和造血成分组成。这些肿瘤通常影响肾上腺，异常表现很少见，文献中描述的病例很少。大多数骨髓脂肪瘤无症状，偶然发现，通过成像测试或尸检。然而,根据病变的位置和大小，骨髓脂肪瘤可引起肿块效应的症状。本文旨在报道一种非常罕见的有症状的原发性骨髓脂肪瘤影响肋骨。
方法：一名21岁的白人女性患者主诉3个月以上的灼热性胸痛，随着强度的逐渐恶化，伴随着右胸壁逐渐增大的隆起。患者接受了第五和第六肋骨的开胸手术，并以安全的边缘完全切除了病变。使用聚丙烯网进行胸壁重建。患者术后病程良好，术后第3天出院。组织病理学检查显示与骨髓脂肪瘤一致的组织学图像。
结论：本报告强调了考虑对肋骨肿瘤块进行髓脂肪瘤诊断的重要性。
方法：一名21岁的白人女性患者主诉3个月以上的灼热性胸痛，随着强度的逐渐恶化，伴随着右胸壁逐渐增大的隆起。患者接受了第五和第六肋骨的开胸手术，并以安全的边缘完全切除了病变。使用聚丙烯网进行胸壁重建。患者术后病程良好，术后第3天出院。组织病理学检查显示与骨髓脂肪瘤一致的组织学图像。
结论：本报告强调了考虑对肋骨肿瘤块进行髓脂肪瘤诊断的重要性。
