Abstract：
OBJECTIVE: Hemophilic pseudotumor (HP) is a very rare complication of hemophilia seen in only 1-2% of the cases. Although it is much more common in long bones, pelvis and small bones of hands and feet and very rarely involving jaw bones.
RESULTS: In the present case, the presence of a rare hemophilic pseudotumor of the mandible with the positive history of Hemophilia B justifies that the history, clinical and radiological examinations were sufficient to arrive at conclusive diagnosis precluding invasive diagnostic procedures such as biopsy hence avoiding the risk of hemorrhage, infection, or fistula. This case also highlights that patient was conservatively managed with Factor IX replacement alone with a very good clinical outcome.
CONCLUSIONS: HP should be considered as a differential diagnosis of any progressive swelling of hard and soft tissues occurring in a patient with severe haemophilia.
RESULTS: In the present case, the presence of a rare hemophilic pseudotumor of the mandible with the positive history of Hemophilia B justifies that the history, clinical and radiological examinations were sufficient to arrive at conclusive diagnosis precluding invasive diagnostic procedures such as biopsy hence avoiding the risk of hemorrhage, infection, or fistula. This case also highlights that patient was conservatively managed with Factor IX replacement alone with a very good clinical outcome.
CONCLUSIONS: HP should be considered as a differential diagnosis of any progressive swelling of hard and soft tissues occurring in a patient with severe haemophilia.
摘要：
目的：血友病假瘤（HP）是一种非常罕见的血友病并发症，仅在1-2％的病例中可见。虽然它在长骨中更常见，骨盆和手脚的小骨头，很少涉及颌骨。
结果：在本例中，存在罕见的下颌骨血友病假瘤，并有乙型血友病阳性病史，临床和放射学检查足以得出决定性的诊断，排除了侵入性诊断程序，例如活检，从而避免了出血的风险。感染,或瘘管。该病例还突出显示,患者单独使用因子IX替代保守管理,具有非常好的临床结果。
结论：HP应被视为严重血友病患者中任何进行性硬组织和软组织肿胀的鉴别诊断。
结果：在本例中，存在罕见的下颌骨血友病假瘤，并有乙型血友病阳性病史，临床和放射学检查足以得出决定性的诊断，排除了侵入性诊断程序，例如活检，从而避免了出血的风险。感染,或瘘管。该病例还突出显示,患者单独使用因子IX替代保守管理,具有非常好的临床结果。
结论：HP应被视为严重血友病患者中任何进行性硬组织和软组织肿胀的鉴别诊断。
