Abstract:
A young woman presented at our clinic with sudden visual loss in the right eye, recurrent vertigo, and right-sided tinnitus. We performed a complete ophthalmological evaluation. This revealed effects of the condition on the small arterioles of the peripheral retina. Susac syndrome is characterized by the clinical triad of retinal arteriolar occlusions, cochleovestibular manifestations, and encephalopathy (which can be identified by neuroimaging abnormalities). Early diagnosis and immunosuppressive therapy improved the patient\'s visual acuity and the remission of her other symptoms. Hemi-central retinal artery occlusion is an atypical neuro-ophthalmological finding in this disease. However, its identification as a sign of Susac syndrome may facilitate timely diagnosis and accurate treatment.
摘要:
一名年轻女子出现在我们的诊所,右眼突然视力丧失,复发性眩晕,和右侧耳鸣.我们进行了完整的眼科评估。这揭示了该病症对周边视网膜的小动脉的影响。Susac综合征的特征是视网膜小动脉阻塞的临床三联征,耳蜗前庭表现,和脑病(可以通过神经影像学异常来识别)。早期诊断和免疫抑制治疗改善了患者的视力和其他症状的缓解。视网膜半中央动脉阻塞是这种疾病的非典型神经眼科发现。然而,将其识别为Susac综合征的标志可能有助于及时诊断和准确治疗。