Abstract：
People with CF (pwCF) are at high risk for malnutrition, making nutritional management a critical aspect of CF care. Over the past several decades, optimal nutritional status for pwCF has been defined by body mass index (BMI) based on evidence linking suboptimal BMI to decreased lung function and life expectancy, although more recent changes in CF care may also bring changes to how nutritional health is defined. The historical focus on weight, BMI, and nutrition as key parts of multidisciplinary CF care starting at an early age places pwCF at increased risk for body image concerns and disordered eating. The landscape of CF care is evolving with the approval of highly effective modulator therapies (HEMT) and resulting improvements in growth; however, issues related to body image and eating remain important to consider, especially as past difficulties gaining weight may shift to discomfort with one\'s weight gain and/or physical appearance. This review aims to describe how body image concerns and disordered eating occur in pwCF across the lifespan; to discuss evidence-based approaches to addressing these concerns; and to identify future directions for research and clinical practice in assessing and treating eating disorders and body image concerns in this population.
摘要：
患有CF（pwCF）的人营养不良的风险很高，使营养管理成为CF护理的一个重要方面。在过去的几十年里，pwCF的最佳营养状况是由体重指数（BMI）定义的，基于将不理想的BMI与肺功能和预期寿命降低联系起来的证据，尽管CF护理的最新变化也可能改变营养健康的定义。历史对体重的关注，BMI,和营养作为从早年开始的多学科CF护理的关键部分，使pwCF在身体形象问题和饮食失调的风险增加。随着高效调节疗法（HEMT）的批准，CF护理的前景正在发展，并导致增长的改善；然而，与身体形象和饮食有关的问题仍然需要考虑，尤其是过去的体重增加困难可能会转变为体重增加和/或身体外观的不适。这篇综述旨在描述整个生命周期中pwCF中的身体形象问题和饮食失调；讨论解决这些问题的循证方法；并确定评估和治疗该人群饮食失调和身体形象问题的未来研究和临床实践方向。
