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Abstract：
Hemophagocytic lymphohistiocytosis (HLH) is an aggressive syndrome of excessive immune activation. It usually occurs in children, mainly during the first year of life. Primary hemophagocytic lymphohistiocytosis is more common and usually occurs in immunocompromised patients. Secondary hemophagocytic lymphohistiocytosis, on the other hand, is less common, especially in immunocompetent patients. Here, we intend to present a case of a 55-year-old male patient who had no known immune deficiency, presented with epistaxis, and was found to have Epstein-Barr virus (EBV)-induced hemophagocytic lymphohistiocytosis.
摘要：
噬血细胞性淋巴组织细胞增生症（HLH）是一种过度免疫激活的侵袭性综合征。它通常发生在儿童身上，主要是在生命的第一年。原发性噬血细胞性淋巴组织细胞增生症更为常见，通常发生在免疫功能低下的患者中。继发性噬血细胞淋巴组织细胞增生症，另一方面,不太常见，尤其是在有免疫能力的患者中。这里,我们打算介绍一个55岁的男性患者，他没有已知的免疫缺陷，出现鼻出血，并被发现患有EB病毒（EBV）诱导的噬血细胞性淋巴组织细胞增生症。
