Mavacamten in Right Ventricular Outflow Tract Obstruction.

Mavacamten 在右心室流出道阻塞中的应用。

• 发表时间: 2024 Jul 17
• 来源期刊: JACC Case Rep
• DOI: 10.1016/j.jaccas.2024.102397
• PMID: 38952423
• 文章类型: Case Reports
• 作者列表: Malhi JK,Carrick RT,Duvall C,Rahman F,Martinez MW,Madrazo J,Barouch LA

关键词: cardiomyopathy; echocardiography; ejection fraction; left ventricle; murmur; right ventricle; treatment

Abstract

Right ventricular outflow tract (RVOT) obstruction is a rare complication of ventricular hypertrophy in patients with hypertrophic cardiomyopathy (HCM). This study presents an unusual case of a patient with HCM with severe RVOT obstruction that was relieved successfully through the use of mavacamten.

摘要

右室流出道（RVOT）阻塞是肥厚型心肌病（HCM）患者心室肥厚的罕见并发症。这项研究提出了一例罕见的HCM患者，该患者患有严重的RVOT梗阻，通过使用mavacampen成功缓解。