PDF(Pubmed)
Abstract：
Congenital ventricular aneurysms (CVA) are rare cardiac anomalies that have been predominantly described in the Black population. They are characterized by an akinetic ventricular protrusion that is commonly located at the basal and apical segments. Although the diagnosis is often incidental and the majority of patients are asymptomatic, life-threatening events such as persistent ventricular arrhythmias, CVA rupture, and heart failure are not uncommon. However, no standardized therapy is currently available and good outcomes have been reported with both conservative and surgical management. We report the cases of two young Black African patients with huge symptomatic CVA lesions who underwent successful surgical repair with a ventricular restoration technique. Both cases were consulted for chest pain and dyspnea. Chest X-ray and transthoracic Doppler echocardiography suggested the diagnosis. Thoracic angioscanner and thoracic magnetic resonance imaging confirmed the diagnosis. Both patients underwent successful surgery. This case report aims to revisit the diagnostic and therapeutic approach to this rare pathology, in our professional environment.
摘要：
先天性心室动脉瘤（CVA）是罕见的心脏异常，主要在黑人人群中有所描述。它们的特征是通常位于基底和顶端段的运动异常的心室突出。尽管诊断通常是偶然的，并且大多数患者无症状，危及生命的事件，如持续性室性心律失常，CVA破裂,心力衰竭并不少见。然而,目前尚无标准化治疗,保守治疗和手术治疗均有良好的结局.我们报告了两名年轻的非洲黑人患者的病例，这些患者有巨大的症状性CVA病变，他们通过心室修复技术成功进行了手术修复。2例均因胸痛和呼吸困难而接受咨询。胸部X线及经胸多普勒超声心动图提示诊断。胸部血管造影和胸部磁共振成像证实了诊断。两名患者均接受了成功的手术。本病例报告旨在重新审视这种罕见病理的诊断和治疗方法。在我们的专业环境中。
