PDF(Pubmed)
Abstract：
BACKGROUND: Fibrosing mediastinitis (FM) is a rare disease characterized by excessive proliferation of fibrous tissue in the mediastinum and can cause bronchial stenosis, superior vena cava obstruction, pulmonary artery and vein stenosis, etc. CASE PRESENTATION: An aging patient with intermittent chest tightness and shortness of breath was diagnosed with FM associated pulmonary hypertension (FM-PH) by echocardiography and enhanced CT of the chest, and CT pulmonary artery (PA)/ pulmonary vein (PV) imaging revealed PA and PV stenosis. Selective angiography revealed complete occlusion of the right upper PV, and we performed endovascular intervention of the total occluded PV. After failure of the antegrade approach, the angiogram revealed well-developed collaterals of the occluded RSPV-V2b, so we chose to proceed via the retrograde approach. We successfully opened the occluded right upper PV and implanted a stent.
CONCLUSIONS: This report may provide new management ideas for the interventional treatment of PV occlusion.
CONCLUSIONS: This report may provide new management ideas for the interventional treatment of PV occlusion.
摘要：
背景：纤维性纵隔炎（FM）是一种罕见的疾病，其特征是纵隔中纤维组织过度增生，可引起支气管狭窄，上腔静脉阻塞,肺动脉和静脉狭窄，等。案例介绍：一位间歇性胸闷和呼吸急促的老年患者通过超声心动图和胸部增强CT诊断为FM相关性肺动脉高压（FM-PH），CT肺动脉（PA）/肺静脉（PV）成像显示PA和PV狭窄。选择性血管造影显示右上肺静脉完全闭塞，我们对总闭塞PV进行了血管内介入治疗。顺行方法失败后，血管造影显示闭塞的RSPV-V2b侧支发育良好，所以我们选择了逆行。我们成功地打开了闭塞的右上PV并植入了支架。
结论：本报告可为肺静脉闭塞的介入治疗提供新的管理思路。
结论：本报告可为肺静脉闭塞的介入治疗提供新的管理思路。
