关键词: complete resection inferior vena cava leiomyosarcoma reconstruction

来  源:   DOI:10.1093/jscr/rjad546   PDF(Pubmed)

Abstract:
Tumors of the inferior vena cava (IVC) are rare and usually malignant and they can be primary and secondary. The most common primary tumor of the IVC is primary leiomyosarcoma. The first case of primary IVC leiomyosarcoma has been described in 1871 [1].The total number of 218 cases has collected until 1996 [2]. After that, three large single center series of these tumors emerged [3-5]. Present a series of five cases of these tumors. All the patients underwent a wide complete resection of tumors and the reconstruction with Dacron grafts. One patient died 19 months after the surgery, while the remaining ones survived without a local and system disease relapse. Although a surgical resection combined with the chemotherapy is often not curative, it can achieve a significant long-term survival. For this reason, we recommend the aggressive surgical management using the modern vascular surgical and oncology techniques.
摘要:
下腔静脉(IVC)的肿瘤很少见,通常是恶性的,可以是原发性和继发性的。IVC最常见的原发性肿瘤是原发性平滑肌肉瘤。第一例原发性IVC平滑肌肉瘤在1871年被描述[1]。截至1996年,共收集了218例[2]。之后,这些肿瘤出现了三个大型单中心系列[3-5]。呈现一系列5例这些肿瘤。所有患者均接受了肿瘤的广泛完整切除并用Dacron移植物进行重建。一名患者在手术后19个月死亡,而其余的幸存下来,没有局部和系统疾病复发。尽管手术切除联合化疗通常无法治愈,它可以实现显著的长期生存。出于这个原因,我们建议使用现代血管外科和肿瘤学技术进行积极的手术治疗.
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