PDF(Pubmed)
Abstract：
Left ventricular noncompaction (LVNC) is commonly described as a congenital cardiomyopathy characterized by prominent myocardial trabeculae and deep intertrabecular recesses extending in the left ventricular chamber. Clinical presentation can differ considerably from asymptomatic individuals to those presenting with heart failure and other serious complications. Diagnosis is usually made by two-dimensional transthoracic echocardiography or cardiac magnetic resonance. Moreover, even if strain parameters are significantly reduced in patients with LVNC, they are not routinely investigated. Here, we report the case of a previously symptomless patient admitted to the hospital for pulmonary edema. Two-dimensional transthoracic echocardiography showed severe valvular heart disease and left ventricle pronounced trabeculation and remodeling, although speckle tracking echocardiography (STE) demonstrated only mild strain reduction. We, therefore, explore the possibility that STE may be useful to differentiate LVNC cardiomyopathy from LVNC phenotype due to severe remodeling.
摘要：
左心室致密化不全（LVNC）通常被描述为先天性心肌病，其特征是突出的心肌小梁和在左心室腔中延伸的深层小梁间凹陷。从无症状个体到出现心力衰竭和其他严重并发症的个体，临床表现可能有很大不同。通常通过二维经胸超声心动图或心脏磁共振进行诊断。此外，即使LVNC患者的应变参数显着降低，他们没有例行调查。这里,我们报告了一例先前因肺水肿入院的无症状患者。二维经胸超声心动图显示严重的心脏瓣膜病和左心室明显的小梁形成和重塑，尽管斑点追踪超声心动图（STE）仅显示轻度应变减少。我们,因此,探讨STE可能有助于区分LVNC心肌病和严重重塑引起的LVNC表型。
