Abstract:
Von Willebrand disease (VWD) is the most common inherited bleeding disorder. It is primarily attributed to malfunctioning or deficient Von Willebrand factor (VWF). Thromboelastography (TEG) has emerged as a valuable tool for assessing coagulation dynamics and guiding transfusion therapy in bleeding patients. Given this, we present a case study of a 23-year-old pregnant female with a past medical history of type 2B VWD, wherein TEG was employed to optimize disease screening and therapy monitoring while minimizing costs and preventing complications associated with low platelet counts. This case underscores the potential utility of TEG in enhancing the care of VWD patients, particularly in unique critical settings such as pregnancy.
摘要:
血管性血友病(VWD)是最常见的遗传性出血性疾病。它主要归因于功能失调或缺乏血管性血友病因子(VWF)。血栓弹力图(TEG)已成为评估凝血动力学和指导出血患者输血治疗的有价值的工具。鉴于此,我们提供了一个案例研究,一个23岁的怀孕女性,有2B型VWD的病史,其中TEG用于优化疾病筛查和治疗监测,同时最小化成本并预防与低血小板计数相关的并发症。这一案例强调了TEG在加强VWD患者护理方面的潜在效用,特别是在独特的关键设置,如怀孕。