PDF(Pubmed)
Abstract：
Retroperitoneal spindle cell neoplasms are diagnostically challenging. Malignant peripheral nerve sheath tumours (MPNSTs) can sometimes present as sporadic primary retroperitoneal tumours. MPNSTs are usually high-grade and highly aggressive tumours and are associated with a poor prognosis. Low-grade MPNSTs are very rarely described. This current case report describes a case of sporadic primary low-grade MPNST presenting as retroperitoneal spindle cell neoplasm. The diagnosis, imaging and immunohistopathological findings, as well as its successful surgical management, are presented.
摘要：
腹膜后梭形细胞肿瘤在诊断上具有挑战性。恶性周围神经鞘瘤（MPNSTs）有时可表现为散发性原发性腹膜后肿瘤。MPNSTs通常是高级别和高度侵袭性的肿瘤，并且预后不良。很少描述低等级MPNST。此最新病例报告描述了一例散发性原发性低度MPNST，表现为腹膜后梭形细胞肿瘤。诊断,影像学和免疫组织病理学发现，以及它成功的手术管理，被呈现。
