%0 Journal Article
%T Low-grade malignant peripheral nerve sheath tumour presenting as retroperitoneal spindle cell neoplasm.
%A Karn M
%A Mahato BK
%A Ojha L
%A Thapa Y
%A Bhatta S
%A Sharma S
%A Chapagain S
%A Ranabhat S
%A Neupane BR
%A Shrestha DM
%J J Int Med Res
%V 52
%N 5
%D 2024 May
%M 38759217
%F 1.573
%R 10.1177/03000605241255504
%X Retroperitoneal spindle cell neoplasms are diagnostically challenging. Malignant peripheral nerve sheath tumours (MPNSTs) can sometimes present as sporadic primary retroperitoneal tumours. MPNSTs are usually high-grade and highly aggressive tumours and are associated with a poor prognosis. Low-grade MPNSTs are very rarely described. This current case report describes a case of sporadic primary low-grade MPNST presenting as retroperitoneal spindle cell neoplasm. The diagnosis, imaging and immunohistopathological findings, as well as its successful surgical management, are presented.