PDF(Pubmed)
Abstract：
Melanotic neuroectodermal tumor of infancy is a rare and usually benign neoplasm occurring in children of young age. This pigmented tumor typically presents in the head and neck region, but other locations may be involved. We report in this article a rare case of a 3-month-old girl presenting with a slowly growing mass localized in the anterior fontanelle. The patient\'s magnetic resonance imaging (MRI) showed a mass extending both extracranial and intracranial, and compressing the adjacent structures. The patient underwent subtotal resection of the mass and a histological study confirmed the diagnosis of melanotic neuroectodermal tumor of infancy. The patient presented later on with a recurrence. An early diagnosis and surgical management for these tumors remain the only guarantees to limit the progression and prevent their recurrence and metastasis.
摘要：
婴儿期黑色素神经外胚层肿瘤是一种罕见且通常发生在年轻儿童中的良性肿瘤。这种色素肿瘤通常出现在头颈部，但可能涉及其他地点。我们在本文中报告了一个3个月大的女孩的罕见病例，该女孩在前font门中出现缓慢增长的肿块。患者的磁共振成像（MRI）显示，颅外和颅内都有肿块，并压缩相邻的结构。该患者接受了肿块的次全切除术，一项组织学研究证实了婴儿期黑色素变性神经外胚层肿瘤的诊断。患者后来出现复发。这些肿瘤的早期诊断和手术治疗仍然是限制进展并防止其复发和转移的唯一保证。
