关键词: biliary cystadenocarcinoma biliary cystadenoma mullerianosis ovarian choristoma

Mesh : Humans Female Adult Diagnosis, Differential Mullerian Ducts / pathology Choristoma / diagnosis pathology Cystadenocarcinoma / diagnosis pathology Lung Neoplasms / diagnosis pathology secondary Liver Neoplasms / diagnosis secondary pathology

来  源:   DOI:10.1177/14782715241247244

Abstract:
Anatomically, normal cells found in an abnormal site are known as choristoma. When any two of the three-cell lineage of the mullerian duct, that is endosalpinx, endocervix and endometrium, are found at an abnormal location, it is termed mullerian choristoma or mullerianosis. Mullerianosis histologically reveals glands of varying sizes lined by cervical, tubal and endometrial cells. Individual cell lineages like endometriosis of the ovary, endosalpingiosis and endocervicosis of the urinary bladder are common. But mullerianosis is quite rare, and as per literature, only about 20 cases have been reported. We report a mullerianosis involving the liver and lung in a 41-year-old female that mimicked metastatic biliary cystadenocarcinoma. It is the first case reported in literature where there is simultaneous involvement of the liver and lung by mullerianosis. The diagnosis was made with the help of histopathology and immunohistochemistry in the resected specimens.
摘要:
解剖学上,在异常部位发现的正常细胞被称为脉络膜瘤。当苗勒管的三细胞谱系中的任何两个时,那是输卵管内膜,宫颈内膜和子宫内膜,在一个异常位置被发现,它被称为苗勒氏脉络膜瘤或苗勒氏病。Mullerianosis组织学上显示不同大小的腺体,由子宫颈排列,输卵管和子宫内膜细胞。单个细胞谱系,如卵巢的子宫内膜异位症,膀胱内膜增生和膀胱内膜增生是常见的。但是穆勒氏症非常罕见,根据文献,仅报告了大约20例。我们报告了一名41岁女性的肝和肺,模仿转移性胆道囊腺癌。这是文献中报道的首例病例,其中肝和肺同时受累。在切除标本的组织病理学和免疫组织化学的帮助下进行诊断。
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