PDF(Pubmed)
Abstract：
Chiari III malformation, a rare and severe subtype of Chiari malformations, is frequently associated with hydrocephalus. The conventional treatment approaches for hydrocephalus in Chiari III malformations have mainly focused on ventriculoperitoneal (VP) shunting, but optimal methods and timing remain uncertain. We report a case of a newborn girl with Chiari III malformation who underwent surgical closure of an occipitocervical encephalocele and ventricular reservoir implantation on her third day of life. This procedure successfully managed her hydrocephalus without significant short-term complications. Three months post-surgery, she developed secondary external hydrocephalus, which was managed through subdural-peritoneal shunting, allowing her to thrive until at least five years of age. This case demonstrates the potential of ventricular reservoir implantation in treating hydrocephalus associated with Chiari III malformation and brings to light secondary external hydrocephalus, subsequently managed by VP shunting.
摘要：
ChiariIII畸形,Chiari畸形的一种罕见且严重的亚型,经常与脑积水有关。ChiariIII畸形脑积水的常规治疗方法主要集中在脑室腹膜（VP）分流上，但最佳方法和时机仍不确定。我们报告了一例患有ChiariIII畸形的新生女孩，该女孩在生命的第三天接受了枕颈脑膨出和心室储液器植入的手术闭合。该手术成功地治疗了她的脑积水，没有明显的短期并发症。手术后三个月,她出现了继发性外部脑积水,这是通过硬膜下-腹膜分流来管理的，让她至少活到五岁.此病例证明了脑室储集器植入治疗与ChiariIII畸形相关的脑积水的潜力，并揭示了继发性外部脑积水。随后由副总裁分流管理。
