关键词: aggressive-fibromatoses chest wall desmoid tumor recurrence

来  源:   DOI:10.1093/jscr/rjae007   PDF(Pubmed)

Abstract:
Desmoid fibromatosis (DF) is a connective tissue tumor that grows aggressively in musculoaponeurotic tissues. It has an annual incidence rate of 2-4/million and is commonly seen in individuals aged 15 to 60 years, with female predominance. While it can occur in any body part, it is commonly found in the extremities, abdominal wall, and abdominal mesentery. But it rarely develops in the chest wall. The cause of the tumor is unknown. However, trauma to the tumor site has been identified in 25% of known cases. The primary treatment is surgical resection. Local recurrence after surgical excision is common. Our study highlights the case of a 12-year-old male patient diagnosed with a desmoid tumor on the chest wall 2 years ago, at the age of 10 years, after mild trauma. The tumor was successfully managed with surgery without radiotherapy treatment and no recurrence was observed in the last 2 years.
摘要:
纤维样纤维瘤病(DF)是一种结缔组织肿瘤,在肌膜膜组织中迅速生长。它的年发病率为2-4/百万,常见于15至60岁的个体,女性占主导地位。虽然它可以发生在身体的任何部位,它常见于四肢,腹壁,和腹部肠系膜.但它很少在胸壁发展。肿瘤的病因未知。然而,在25%的已知病例中发现了肿瘤部位的创伤。主要治疗是手术切除。手术切除后局部复发很常见。我们的研究强调了一名12岁的男性患者,2年前被诊断为胸壁纤维瘤,在10岁的时候,轻度创伤后.在没有放射治疗的情况下,通过手术成功治疗了肿瘤,并且在过去的2年中没有观察到复发。
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