Subcutaneous panniculitis-like T-cell lymphoma: fever and facial swelling with hemophagocytic syndrome.

皮下脂膜炎样 T 细胞淋巴瘤: 发热和面部肿胀伴噬血细胞综合征.

• 发表时间: 2024 Apr 2
• 来源期刊: BMJ Case Rep
• DOI: 10.1136/bcr-2023-256615
• PMID: 38569732
• 文章类型: Case Reports
• 作者列表: Aggarwal S,Narayan A,Agarwal S,Wig N

关键词: Haematology (incl blood transfusion); Malignant and Benign haematology; Medical management; Skin cancer

Mesh: Male; Humans; Lymphohistiocytosis, Hemophagocytic / diagnosis drug therapy etiology; Panniculitis / diagnosis drug therapy etiology; Lymphoma, T-Cell / complications diagnosis drug therapy; Skin / pathology; Angioedema / pathology; Fever / etiology

Abstract

We report a case of subcutaneous panniculitis-like T-cell lymphoma (SPTCL) in a young man presenting with fever and facial swelling. He had pancytopenia and hemophagocytic syndrome (HPS) on evaluation. The histopathological examination of skin punch biopsy from the face and chest wall showed SPTCL. Given the associated HPS, he was started on steroid and multidrug chemotherapy following which he had symptomatic improvement.

摘要

我们报告了一例发烧和面部肿胀的年轻人皮下脂膜炎样T细胞淋巴瘤（SPTCL）。他在评估时患有全血细胞减少症和噬血细胞综合征（HPS）。面部和胸壁皮肤穿刺活检的组织病理学检查显示为SPTCL。鉴于相关的HPS，他开始接受类固醇和多药化疗，随后症状有所改善。