Abstract：
The characteristics of the pulmonary cysts on the high-resolution computed tomography (HRCT) chest images are an important diagnostic clue to distinguish among cystic lung diseases. The diagnostic accuracy of HRCT was reported to be as high as 90% by experienced pulmonologists and radiologists. Herein, we report the case of an elderly woman with Birt-Hogg-Dubé syndrome (BHDS) whose HRCT images displayed lymphangioleiomyomatosis-like features of the pulmonary cysts, rendering it difficult for us to diagnose BHDS. This case illustrates the significance of a thorough anamnesis, physical examination, and skin biopsy of facial papules to establish an accurate diganosis.
摘要：
高分辨率计算机断层扫描（HRCT）胸部图像上的肺囊肿特征是区分囊性肺病的重要诊断线索。据经验丰富的肺科医师和放射科医师报告，HRCT的诊断准确性高达90％。在这里，我们报告了一位患有Birt-Hogg-Dubé综合征（BHDS）的老年妇女的病例，其HRCT图像显示了肺囊肿的淋巴管平滑肌瘤病样特征，使我们难以诊断BHDS。这个案例说明了彻底回忆的重要性，体检,并对面部丘疹进行皮肤活检以建立准确的头盖病。
