关键词: Aneurysmal bone cyst Follow-up Pediatric Thoracic spine

来  源:   DOI:10.25259/SNI_886_2023   PDF(Pubmed)

Abstract:
UNASSIGNED: Spinal aneurysmal bone cysts (ABCs) are rare, histologically benign tumors with aggressive behavior, which may cause bone and soft-tissue destruction, particularly affecting neural elements. Management of these tumors, including treatment modalities and follow-up protocols, remains challenging.
UNASSIGNED: A 7-year-old boy presented with chest wall pain persisting for two months before admission, accompanied by progressive mono paresis lasting ten days before admission. Myelopathy signs were evident during the examination. Imaging confirmed a multicystic lesion at the T6 level involving the posterior elements of the vertebra, with significant cord compression. Due to deteriorating neurological function, he underwent urgent laminectomy and neural decompression, followed by subtotal tumor resection. Postoperative histopathological examination confirmed the diagnosis of an ABC, and the patient experienced significant neurological recovery. However, after 21 days, the patient was readmitted to the emergency department with severe paraparesis. Magnetic resonance imaging revealed rapid growth of the residual tumor, leading to cord compression. He underwent aggressive total tumor resection, T6 vertebral body corpectomy, and fixation with pedicle screws and cage insertion. Following the second surgery, prompt neurological recovery occurred.
UNASSIGNED: This rare case report emphasizes the importance of a close follow-up protocol for spinal ABCs in the pediatric population. It highlights the challenges in managing these tumors and the need for vigilant monitoring to detect and address rapid recurrences.
摘要:
脊柱动脉瘤性骨囊肿(ABC)很少见,组织学上的良性肿瘤具有攻击行为,这可能会导致骨骼和软组织的破坏,特别是影响神经元素。这些肿瘤的管理,包括治疗方式和后续方案,仍然具有挑战性。
一名7岁男孩在入院前出现胸壁疼痛持续两个月,在入院前10天伴有进行性单纯性轻瘫。检查期间脊髓病征象明显。影像学检查证实了T6级多囊性病变,涉及椎骨的后部元素,有明显的脊髓压缩。由于神经功能恶化,他接受了紧急椎板切除术和神经减压术,其次是肿瘤次全切除。术后组织病理学检查证实了ABC的诊断,患者经历了显著的神经系统恢复。然而,21天后,患者因重度轻瘫再次进入急诊科。磁共振成像显示残留肿瘤快速生长,导致绳索压缩。他接受了积极的全肿瘤切除术,T6椎体全切术,用椎弓根螺钉和笼子插入固定。第二次手术后,迅速恢复神经系统。
这份罕见病例报告强调了在儿科人群中对脊柱ABC进行密切随访的重要性。它强调了管理这些肿瘤的挑战,以及需要警惕监测以检测和解决快速复发。
公众号