Abstract：
The aim of this study was to evaluate the postoperative course and long-term functional and aesthetic outcomes in patients with Beckwith-Wiedemann syndrome (BWS) following surgical reduction of macroglossia, using multiple questionnaires. Patients with BWS who underwent keyhole reduction for macroglossia were included in this study. The postoperative course for each patient was recorded, and multiple questionnaires were administered to evaluate aesthetic concerns, oral incompetence or feeding difficulties, sleep-disordered breathing symptoms, and speech. Nine patients underwent ten reduction glossoplasty surgeries. The mean age at surgery was 22 months. The postoperative course for each case was uneventful, except for one patient who had wound dehiscence. The questionnaires revealed significant improvements in tongue appearance, feeding, drooling, facial appearance, and psychosocial outcomes. There was also a significant reduction in sleep-disordered breathing symptoms after surgery. Keyhole reduction glossoplasty is a safe and effective procedure for the treatment of macroglossia in BWS patients, with excellent functional and aesthetic outcomes and a low complication rate.
摘要：
这项研究的目的是评估Beckwith-Wiedemann综合征（BWS）患者在手术减少巨舌后的术后病程和长期功能和美学结果，使用多个问卷。这项研究包括接受锁孔减少术治疗巨舌的BWS患者。记录每位患者的术后病程，并进行了多次问卷调查以评估美学问题，口腔机能不全或进食困难，睡眠呼吸紊乱的症状,和演讲。9例患者接受了十例复位舌肌成形术。手术时的平均年龄为22个月。每个病例的术后过程都很顺利，除了一个伤口裂开的病人.问卷显示舌头外观有显著改善，喂养,流口水,面部外观,和心理社会结果。手术后睡眠呼吸紊乱症状也显著减少。锁孔复位舌肌成形术是治疗BWS患者巨大舌肌的一种安全有效的方法，具有出色的功能和美学效果，并发症发生率低。
