关键词: Pulmonary alveolar microlithiasis Pulmonary hypertension Right heart catheterization

Mesh : Humans Calcinosis Genetic Diseases, Inborn Hypertension, Pulmonary / diagnosis etiology therapy Lung Diseases Prospective Studies Pulmonary Alveoli Retrospective Studies Review Literature as Topic

来  源:   DOI:10.1016/j.cpcardiol.2024.102492

Abstract:
This letter commends the study \"Severe pulmonary hypertension in pulmonary alveolar microlithiasis: A comprehensive literature review\" for its thorough exploration of Pulmonary Alveolar Microlithiasis (PAM) and its association with pulmonary hypertension (PH). The study offers insights into PAM\'s genetics, clinical manifestations, diagnostic approaches, and treatment modalities. It highlights the importance of early diagnosis and management while discussing limitations such as its retrospective nature and small sample size. Despite these limitations, the study contributes significantly to understanding PAM and PH, emphasizing the need for larger prospective studies to validate findings and explore novel therapeutic avenues.
摘要:
这封信赞扬研究“肺泡微石症中的严重肺动脉高压:全面的文献综述”,以彻底探索肺泡微石症(PAM)及其与肺动脉高压(PH)的关系。这项研究提供了对PAM遗传学的见解,临床表现,诊断方法,和治疗方式。它强调了早期诊断和管理的重要性,同时讨论了其回顾性性质和小样本量等局限性。尽管有这些限制,这项研究对理解PAM和PH有重要贡献,强调需要更大的前瞻性研究来验证研究结果并探索新的治疗途径。
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