PDF(Pubmed)
Abstract：
Intralabyrinthine schwannomas (ILSs) are rare tumors involving the otic capsule. Notably, they are often misdiagnosed because their symptoms mimic those of other, more common inner ear pathologies. Diagnosis requires high-resolution contrast-enhanced magnetic resonance imaging (MRI), which reveals filling defects (using a T2-weighted MRI sequence) or focal enhancement (using a T1-weighted MRI sequence with gadolinium enhancement) in the inner ear. A 52-year-old male patient with intractable vertigo or single-sided deafness should raise suspicion of this clinical entity as a differential diagnosis. Translabyrinthine excision of the tumor along with auditory rehabilitation using a cochlear implant can provide good outcomes with minimal morbidity in carefully selected cases. Here, we present an interesting case of a transmodiolar ILS mimicking Meniere\'s disease, wherein surgery using the translabyrinthine approach and an extended cochleostomy yielded favorable outcomes.
摘要：
丙流内神经鞘瘤（ILS）是涉及耳囊的罕见肿瘤。值得注意的是,他们经常被误诊，因为他们的症状与其他人的症状相似，更常见的内耳病变。诊断需要高分辨率对比增强磁共振成像(MRI),这揭示了内耳的填充缺陷（使用T2加权MRI序列）或局灶性增强（使用T1加权MRI序列和钆增强）。患有顽固性眩晕或单侧耳聋的52岁男性患者应怀疑该临床实体作为鉴别诊断。在精心选择的病例中，经迷宫切除肿瘤以及使用耳蜗植入物进行听觉康复可以提供良好的结果，并且发病率最低。这里,我们提出了一个有趣的案例，模拟梅尼埃病，其中使用经迷路入路和延长的耳蜗造口术的手术产生了良好的结果。
