Abstract：
Objective: Behavioral variant frontotemporal dementia (bvFTD) is a neurodegenerative condition characterized by progressive changes in behavior, cognition, and day-to-day functioning. Progression of the disease usually leads to death 3-5 years after diagnosis. However, there are reports of individuals who are initially diagnosed with bvFTD but fail to progress. These individuals are thought to have what is becoming known as phenocopy bvFTD (phFTD). Methods: This manuscript reviews a single case study of a 68-year-old male Veteran who was diagnosed with bvFTD in 2010, which has not progressed over time. Results: Review of serial neuropsychological evaluations was broadly normal with mild evidence of executive dysfunction with minimal reliable change in his performances from 2015, 2017, and 2022 evaluations. He also has not developed neuroimaging evidence of FTD. Conclusions: This case illustrates the importance of monitoring individuals over time and incorporating neuroimaging data into the diagnosis. We believe this Veteran\'s presentation is most consistent with what has been described as phFTD.
摘要：
目的：行为变异额颞叶痴呆（bvFTD）是一种神经退行性疾病，其特征是行为的进行性改变，认知，和日常运作。疾病的进展通常导致诊断后3-5年死亡。然而,有报告称最初诊断为bvFTD但未能进展的个体.这些人被认为具有所谓的表型bvFTD（phFTD）。方法：本手稿回顾了一个68岁的男性退伍军人在2010年被诊断为bvFTD的单个案例研究，该研究没有随着时间的推移而进展。结果：从2015年，2017年和2022年的评估中，对连续神经心理学评估的回顾大致正常，有轻度执行功能障碍的证据，其表现的可靠变化最小。他也没有发现FTD的神经影像学证据。结论：此病例说明了随时间监测个体并将神经影像学数据纳入诊断的重要性。我们相信这位退伍军人的演讲与phFTD的描述最为一致。
