Abstract：
Contracturing granulomatous myositis is a rare myopathy in which patients present with flexion contractures of the upper limbs in addition to slowly progressive muscle weakness and pain. Whether it represents a distinct nosological entity remains a point of discussion. We present a patient with isolated granulomatous disease of the muscle that responded very well to intravenous immunoglobulins after treatment failure of corticosteroids and methotrexate.
摘要：
挛缩性肉芽肿性肌炎是一种罕见的肌病，患者除了缓慢进行性肌肉无力和疼痛外，还表现为上肢屈曲挛缩。它是否代表一个独特的nosological实体仍然是一个讨论的焦点。我们介绍了一名患有孤立性肌肉肉芽肿病的患者，该患者在皮质类固醇和甲氨蝶呤治疗失败后对静脉内免疫球蛋白的反应非常好。
