PDF(Pubmed)
Abstract：
Intraluminal tumor in the azygos vein is a rare disease that can cause superior vena cava (SVC) syndrome. Radiotherapy and endovascular stenting with or without chemotherapy are reported to have a high clinical success rate for the management of SVC syndrome with malignancy, but a poor survival rate. Here, we report a 69-year-old man who presented with swelling of the face and upper extremities, who was diagnosed with SVC syndrome caused by an intraluminal tumor in the azygos vein. Enhanced chest computed tomography revealed an intraluminal mass with a filling defect from the azygos vein to the SVC, with no extravascular extension or dissemination of the primary tumor. Surgical resection of the mass en bloc with the azygos vein and SVC reconstruction was performed. A poorly differentiated carcinoma was diagnosed on postoperative pathological evaluation. Twelve months after resection, the patient was well with no signs of recurrent disease. This case highlights that surgical resection should be considered as a treatment of choice for the management of SVC syndrome caused by an intraluminal malignancy in the azygos vein.
摘要：
奇静脉腔内肿瘤是一种罕见的疾病，可惹起上腔静脉（SVC）综合征。据报道，有或没有化疗的放射治疗和血管内支架置入术对SVC综合征伴恶性肿瘤的治疗具有很高的临床成功率。但存活率很低。这里,我们报道了一名69岁的男子面部和上肢肿胀，他被诊断为由奇静脉腔内肿瘤引起的SVC综合征。增强胸部计算机断层扫描显示管腔内肿块，从奇静脉到SVC有充盈缺损，没有血管外延伸或原发肿瘤播散。用奇静脉和SVC重建手术切除肿块。术后病理评估诊断为低分化癌。切除后12个月,患者病情良好，没有疾病复发的迹象。此病例突出表明，手术切除应被视为治疗由奇静脉腔内恶性肿瘤引起的SVC综合征的一种选择。
