关键词: Amniotic bands syndrome Case report Plastic surgery Syndactyly Upper extremity Z-plasty

来  源:   DOI:10.1016/j.ijscr.2024.109277   PDF(Pubmed)

Abstract:
BACKGROUND: Amniotic band syndrome is a fetal entrapment in strands of amniotic tissue. This condition causes multiple deformities ranging from simple constricting bands to lymphedema, autoamputation, syndactyly and other congenital anomalies. Reconstructive surgery is the main treatment for ABS.
METHODS: A 4-year-old male presented with multiple constricting bands affecting both hands in addition to an incomplete syndactyly between the third and fourth left digits. A two-staged operation was performed to repair the deformities with 6 months interval. Series of Z-plasties were used to release the constricting bands and the syndactyly was separated by a web zigzag incision approach and full-thickness skin grafting.
CONCLUSIONS: Management of ABS must be individualized. The urgency of the surgical release depends on the depth of the constricting bands and their influence on circulation and lymphatic drainage. Superficial bands can be released electively for cosmetic appearance while deep bands should be released as soon as possible. The separation of syndactyly should be done at the first year of life to maintain the digits functionality and parallel growth.
CONCLUSIONS: This paper emphasizes the importance of early repair of constricting bands associated with syndactyly to avoid the consequences of the delay on digital growth.
摘要:
背景:羊膜带综合征是一种羊膜组织的胎儿包陷。这种情况会导致多种畸形,从简单的收缩带到淋巴水肿,自动截肢,并肢和其他先天性异常。修复手术是ABS的主要治疗方法。
方法:一名4岁男性,除了左三指和左指四指之间不完整的连音外,还表现出多条收缩带影响双手。进行了两个阶段的手术,以6个月的间隔修复畸形。使用一系列Z型塑料来释放收缩带,并通过网状之字形切口方法和全层皮肤移植来分离。
结论:ABS的管理必须个体化。手术释放的紧迫性取决于收缩带的深度及其对循环和淋巴引流的影响。可以选择性地释放表面带,以用于美容外观,同时应尽快释放深层带。syndactyly的分离应在生命的第一年进行,以保持数字功能和并行增长。
结论:本文强调了早期修复与齐指相关的收缩带的重要性,以避免数字生长延迟的后果。
公众号