Abstract：
Aneurysmal bone cyst (ABC) is a rare and usually painful condition, representing about 1% of all bone tumors. A geographical lytic, expansile, and septated radiological pattern, with fluid-fluid levels on MRI, is classically displayed. ABC can be a primary bone lesion (70% of patients) or can arise in an underlying condition and is subsequently named \"ABC-like changes\" (30%). ABC-like changes are more frequently encountered in skeletal segments affected by chondroblastoma, fibrous dysplasia, giant cell tumor, osteoblastoma, non-ossifying fibroma, and osteosarcoma. In this article, we describe the first case of ABC-like changes developed in association with an ultra-rare sclerosing bone disease: melorheostosis. Melorheostosis is characterized by recognizable patterns on radiological studies with a pathological increased bone density and a cortical thickening within the periosteal or endosteal space, usually with a \"dripping candle wax\" appearance. More rarely, other different radiological patterns can be observed, such as \"osteopatia striata-like,\" \"osteoma-like,\" \"myositis ossificans-like,\" and mixed patterns. Pain and limb hypotrophy are the most common clinical manifestations. We report the case of a Caucasian male with a clinic-radiological diagnosis of melorheostosis (with epiphyseal osteopoikilosis) since the age of twelve. At the age of nineteen, he suffered from increased pain in the proximal right thigh, and the radiological control revealed an expansive septated lesion at the right proximal femoral bone. The diagnosis of ABC-like changes developed in melorheostosis was obtained after CT-guided bone biopsy and confirmed by open-incisional biopsy.
摘要：
动脉瘤性骨囊肿（ABC）是一种罕见且通常疼痛的疾病，约占所有骨肿瘤的1%。一个地理抒情者，膨胀性,和隔离的放射学模式，MRI上的流体水平，经典显示。ABC可能是原发性骨病变（70％的患者），也可能出现在潜在疾病中，随后被命名为“ABC样变化”（30％）。在受软骨母细胞瘤影响的骨骼节段中，更经常遇到ABC样的变化，纤维发育不良,巨细胞瘤,成骨细胞瘤,非骨化性纤维瘤,和骨肉瘤.在这篇文章中,我们描述了首例与超罕见的硬化性骨病相关的ABC样改变:恶性骨病。Melorheososis的特征是放射学研究中可识别的模式，具有病理性增加的骨密度和骨膜或骨内膜间隙内的皮质增厚。通常带有“滴蜡烛蜡”的外观。很少,可以观察到其他不同的放射学模式，如“纹状体样骨膜”，\"\"骨瘤样，骨化性肌炎，“和混合模式。疼痛和肢体肥大是最常见的临床表现。我们报告了一名白人男性，自12岁起就进行了临床放射学诊断为恶性骨病（伴有骨phy骨骨质疏松）。在19岁的时候，他的右大腿近端疼痛加剧，放射学对照显示右侧股骨近端有一个扩张性的分隔性病变。在CT引导下进行骨活检并通过开放切开活检证实后，可以诊断出恶性骨病中发生的ABC样变化。
