Abstract：
This study presents the clinical characteristics, imaging manifestations, and surgical experience in 38 patients diagnosed with craniofacial fibrous dysplasia in fronto-orbital region (foFD).
We retrospectively analyzed the clinical data from 38 patients who had surgery for foFD. The surgical procedure typically involved extensive tumor removal, followed by immediate reconstruction of the frontal bone and orbit using synthetic materials. Additionally, 9 patients underwent simultaneous microscopic decompression of the optic canal.
Common clinical manifestations included progressive fronto-orbital bone deformity (35), proptosis (28), orbital dystopia (21), and visual impairment (9). The disease primarily affecting the frontal bone (38), the sphenoid bone (28), and the ethmoid bone (24). The optic canal was involved in 9 patients with functional impairment. Computed tomography scans in all 38 cases revealed satisfactory repair material positioning and complete resolution of frontal deformities. Among the 9 patients who underwent optic canal decompression, 7 experienced partial recovery of visual acuity after surgery.
In the surgical treatment of foFD, it is crucial to achieve maximal bone resection and repair skull defects, while decompressing the optic canal can provide significant benefits for patients with decreased visual function preoperatively. The use of preformed artificial materials offers advantages in aesthetic restoration after lesion excision.
We retrospectively analyzed the clinical data from 38 patients who had surgery for foFD. The surgical procedure typically involved extensive tumor removal, followed by immediate reconstruction of the frontal bone and orbit using synthetic materials. Additionally, 9 patients underwent simultaneous microscopic decompression of the optic canal.
Common clinical manifestations included progressive fronto-orbital bone deformity (35), proptosis (28), orbital dystopia (21), and visual impairment (9). The disease primarily affecting the frontal bone (38), the sphenoid bone (28), and the ethmoid bone (24). The optic canal was involved in 9 patients with functional impairment. Computed tomography scans in all 38 cases revealed satisfactory repair material positioning and complete resolution of frontal deformities. Among the 9 patients who underwent optic canal decompression, 7 experienced partial recovery of visual acuity after surgery.
In the surgical treatment of foFD, it is crucial to achieve maximal bone resection and repair skull defects, while decompressing the optic canal can provide significant benefits for patients with decreased visual function preoperatively. The use of preformed artificial materials offers advantages in aesthetic restoration after lesion excision.
摘要：
目的：本研究提出了临床特征，影像学表现,38例诊断为额眶区（foFD）颅面纤维发育不良（CFD）患者的手术经验。
方法：我们回顾性分析了38例foFD手术患者的临床资料。外科手术通常涉及广泛的肿瘤切除，然后使用合成材料立即重建额骨和眼眶。此外,9例患者同时行视神经管显微减压术。
结果：常见临床表现包括进行性额眶骨畸形（35），突增（28），眼眶反乌托邦（21），视力障碍（9）。主要影响额骨的疾病（38），蝶骨(28)和筛骨(24)。9例功能障碍患者受累视神经管。所有38例患者的CT扫描均显示修复材料定位满意，额叶畸形完全消退。在接受视神经管减压术的9例患者中，7术后阅历了部分视力恢复。
结论：在foFD的手术治疗中，实现最大程度的骨切除和修复颅骨缺损至关重要，而减压视神经管可以为术前视觉功能下降的患者提供显著的益处。预制人造材料的使用在病灶切除后的美学修复方面具有优势。
方法：我们回顾性分析了38例foFD手术患者的临床资料。外科手术通常涉及广泛的肿瘤切除，然后使用合成材料立即重建额骨和眼眶。此外,9例患者同时行视神经管显微减压术。
结果：常见临床表现包括进行性额眶骨畸形（35），突增（28），眼眶反乌托邦（21），视力障碍（9）。主要影响额骨的疾病（38），蝶骨(28)和筛骨(24)。9例功能障碍患者受累视神经管。所有38例患者的CT扫描均显示修复材料定位满意，额叶畸形完全消退。在接受视神经管减压术的9例患者中，7术后阅历了部分视力恢复。
结论：在foFD的手术治疗中，实现最大程度的骨切除和修复颅骨缺损至关重要，而减压视神经管可以为术前视觉功能下降的患者提供显著的益处。预制人造材料的使用在病灶切除后的美学修复方面具有优势。
