PDF(Pubmed)
Abstract：
UNASSIGNED: Systemic sclerosis (SSc) is divided into three subtypes: limited cutaneous SSc (lcSSc), diffuse cutaneous SSc (dcSSc), and systemic sclerosis sine scleroderma (ssSSc). ssSSc is a rare subtype of SSc that presents with internal organ manifestations but no cutaneous findings.
UNASSIGNED: We report the case of a 58-year-old patient with a history of pulmonary hypertension who presented with symptoms of fatigue, inflammatory polyarthritis, and joint swelling. Following a comprehensive clinical examination and laboratory tests, the patient was diagnosed with ssSSc.
UNASSIGNED: Due to its atypical clinical course, we present this case report, which commenced with idiopathic pulmonary hypertension. Subsequently, after 7 months, the patient presented complaints of polyarthritis with positive antinuclear antibodies. Raynaud\'s phenomenon was identified 2 months later during the rheumatology clinic examination. Typically, the clinical course encompasses all three features simultaneously, without any gap between them.
UNASSIGNED: Diagnosis of ssSSc remains challenging, and it is essential to consider this disease form in all cases involving unexplained fibrotic involvement of the internal organs.
UNASSIGNED: We report the case of a 58-year-old patient with a history of pulmonary hypertension who presented with symptoms of fatigue, inflammatory polyarthritis, and joint swelling. Following a comprehensive clinical examination and laboratory tests, the patient was diagnosed with ssSSc.
UNASSIGNED: Due to its atypical clinical course, we present this case report, which commenced with idiopathic pulmonary hypertension. Subsequently, after 7 months, the patient presented complaints of polyarthritis with positive antinuclear antibodies. Raynaud\'s phenomenon was identified 2 months later during the rheumatology clinic examination. Typically, the clinical course encompasses all three features simultaneously, without any gap between them.
UNASSIGNED: Diagnosis of ssSSc remains challenging, and it is essential to consider this disease form in all cases involving unexplained fibrotic involvement of the internal organs.
摘要：
■系统性硬化症（SSc）分为三种亚型：有限的皮肤SSc（lcSSc），弥漫性皮肤SSc（dcSSc），和系统性硬化症硬皮病（ssSSc）。ssSSc是一种罕见的SSc亚型，表现为内脏器官表现，但没有皮肤表现。
我们报告了一例58岁的肺动脉高压患者，有疲劳症状，炎性多发性关节炎，关节肿胀.经过全面的临床检查和实验室检查，患者被诊断为ssSSc。
■由于其非典型的临床病程，我们提供这个病例报告,从特发性肺动脉高压开始。随后，7个月后,患者主诉多关节炎,抗核抗体阳性.2个月后在风湿病门诊检查中发现了雷诺现象。通常,临床过程同时包含所有三个特征，他们之间没有任何差距。
■ssSSc的诊断仍然具有挑战性，在所有涉及内脏器官无法解释的纤维化受累的病例中，必须考虑这种疾病形式。
我们报告了一例58岁的肺动脉高压患者，有疲劳症状，炎性多发性关节炎，关节肿胀.经过全面的临床检查和实验室检查，患者被诊断为ssSSc。
■由于其非典型的临床病程，我们提供这个病例报告,从特发性肺动脉高压开始。随后，7个月后,患者主诉多关节炎,抗核抗体阳性.2个月后在风湿病门诊检查中发现了雷诺现象。通常,临床过程同时包含所有三个特征，他们之间没有任何差距。
■ssSSc的诊断仍然具有挑战性，在所有涉及内脏器官无法解释的纤维化受累的病例中，必须考虑这种疾病形式。
