PDF(Pubmed)
Abstract：
Vulvar leiomyomas are extremely rare smooth muscle tumors that are easily mistaken for other lesions, as the differential diagnosis must consider a wide spectrum of benign and malignant lesions. We present the case of a 52-year-old woman with a three-year history of progressive abdominal distension and pain and an enlarging vulvar mass distorting the labia majora and causing gait disturbance. Imaging confirmed an enormous pelvic mass originating in the uterus, compatible with a leiomyoma/sarcoma, and large perineal and vulvar masses with similar characteristics. Histopathology after surgical removal revealed benign abdominal, vulvar, and perineal leiomyomas. This case highlights the rarity and diagnostic challenges of extra-uterine leiomyomas, particularly those in the vulvar region.
摘要：
外阴平滑肌瘤是极其罕见的平滑肌肿瘤，很容易被误认为是其他病变，因为鉴别诊断必须考虑广泛的良性和恶性病变。我们介绍了一名52岁妇女的病例，该妇女有三年的进行性腹胀和疼痛史，外阴肿块扩大，扭曲了大阴唇并引起步态障碍。影像学证实一个巨大的盆腔肿块起源于子宫，与平滑肌瘤/肉瘤相容，以及具有相似特征的会阴和外阴大肿块。手术切除后的组织病理学显示腹部良性，外阴,会阴平滑肌瘤.该病例突出了子宫外平滑肌瘤的罕见性和诊断挑战，尤其是外阴区的。
