关键词: Alveolar soft part sarcoma Female genital tract Prognosis TFE3 Uterine corpus

Mesh : Female Humans Adult Follow-Up Studies Sarcoma, Alveolar Soft Part / diagnosis surgery Uterus Conservative Treatment Perineum

来  源:   DOI:10.1016/j.tjog.2023.07.025

Abstract:
OBJECTIVE: Female genital alveolar soft part sarcoma (ASPS) is rare and has a favourable prognosis compared to ASPS from other sites. We reported our experience to manage a case with uterine corpus ASPS (UC ASPS) and conducted a literature review on prognosis of ASPS from different sites of female genital tract.
METHODS: This report represented a 33-year-old woman who had UC ASPS. She received tumor excision with uterine preservation and had the longest follow-up time (155 months) without recurrence in the literature.
CONCLUSIONS: UC ASPS has better prognosis than ASPS from the uterine cervix, the low uterine segment, vulvovaginal area and perineum. We recommended conservative treatment for young women with UC ASPS.
摘要:
目的:女性生殖器肺泡软组织肉瘤(ASPS)罕见,与其他部位的ASPS相比,预后良好。我们报告了我们处理子宫体ASPS(UCASPS)病例的经验,并对女性生殖道不同部位ASPS的预后进行了文献综述。
方法:本报告为一名33岁女性,患有UCASPS。她接受了保留子宫的肿瘤切除术,随访时间最长(155个月),没有复发。
结论:UCASPS的预后优于宫颈ASPS,子宫下段,外阴阴道区和会阴.我们建议对患有UCASPS的年轻女性进行保守治疗。
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