Abstract：
Sagittal suture synostosis is one of the most common craniosynostoses and is often diagnosed by characteristic narrow and long skull shape, scaphocephaly. However, some patients with sagittal suture synostosis do not present with typical scaphocephaly, making early diagnosis difficult. In this study, five cases of characteristic skull deformity showing a narrowing of the cranium posterior to the coronal suture on computed tomography (CT) are presented. The three older children presented with papilledema and intellectual disability and a closed sagittal suture on CT. The two infant cases were diagnosed with the characteristic cranial deformities with aggravation of the deformity over time, but sagittal suture closure was not evident on CT. All patients underwent cranial remodeling surgery. In the two infant cases, the histopathological findings showed that the anterior part of the sagittal suture was firmly fused with fibrous tissue without bony fusion. These findings suggested that narrowing of the cranium posterior to the coronal suture might be due to functional fusion of the anterior portion of the sagittal suture prior to bony fusion. In an infant presenting with such a deformity that shows aggravation of the deformity over time, surgical treatment should be considered.
摘要：
矢状缝线滑膜是最常见的颅骨滑膜之一，通常通过特征性的狭窄和长颅骨形状来诊断。头颅。然而,一些矢状面缝线滑脱症患者不存在典型的头颅肩,使早期诊断变得困难。在这项研究中,提出了5例特征性颅骨畸形，在计算机断层扫描（CT）上显示冠状缝合线后方的颅骨变窄。三名年龄较大的儿童在CT上表现为乳头水肿和智力障碍，并有闭合的矢状缝线。这两个婴儿病例被诊断为特征性的颅骨畸形，随着时间的推移，畸形加重，但CT显示矢状缝线闭合不明显。所有患者均接受颅骨重塑手术。在这两个婴儿案例中，组织病理学发现，矢状缝线的前部与纤维组织牢固融合，无骨融合。这些发现表明，冠状缝线后方的颅骨变窄可能是由于在骨融合之前矢状缝线的前部功能性融合所致。在出现这种畸形的婴儿中，随着时间的推移，畸形加剧，应考虑手术治疗。
