Abstract：
Hypertrophic pachymeningitis (HP) is a relatively rare disease of the central nervous system characterized by local or diffuse fibrous thickening of the dura mater. At present, there is still insufficient research on the pathogenesis and treatment strategies of this disease. We reported a continuous case series of seven patients with idiopathic HP (IHP), and also details one case of immunoglobulin G4-related HP requiring surgical intervention. Early diagnosis and appropriate surgical intervention for IHP could prevent the progression of permanent neurological damage and spinal cord paraplegia.
摘要：
肥厚性硬脑膜炎（HP）是一种相对罕见的中枢神经系统疾病，其特征是硬脑膜的局部或弥漫性纤维增厚。目前,目前对该病的发病机制和治疗策略的研究还不足。我们报道了一个由7例特发性HP（IHP）患者组成的连续病例系列，并详细介绍了1例需要手术干预的免疫球蛋白G4相关HP。IHP的早期诊断和适当的手术干预可以预防永久性神经损伤和脊髓截瘫的进展。
