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Abstract：
Pancreatic acinar cell carcinoma (PACC) is a rare pancreatic malignancy with unique clinical, molecular, and morphologic features. The long-term survival of patients with PACC is substantially better than that of patients with ductal adenocarcinoma of the pancreas. Surgical resection is considered the first choice for treatment; however, there is no standard treatment option for patients with inoperable disease. The patient with metastatic PACC reported herein survived for more than 5 years with various treatments including chemotherapy, radiotherapy, antiangiogenic therapy and combined immunotherapy.
摘要：
胰腺腺泡细胞癌(PACC)是一种罕见的胰腺恶性肿瘤,分子，和形态学特征。PACC患者的长期生存率明显优于胰腺导管腺癌患者。手术切除被认为是治疗的首选；然而，对于无法手术的患者，没有标准的治疗选择。本文报道的转移性PACC患者在包括化疗在内的各种治疗下存活超过5年。放射治疗,抗血管生成治疗和联合免疫疗法。
